A.I. BURNASYAN FMBC CLINICAL BULLETIN

ISSN 2782-6430 (print)

State Research Center −Burnasyan Federal Medical Biophysical
Center of Federal Medical Biological Agency

The journal is published in Russian.
Format – A4.
The periodicity of the journal is 4 times a year.

Issue №2 2025 год

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A.I. Burnasyan  FMBC clinical bulletin. 2023 № 4

A.A. Slusar1, K.V. Vetkova2

Budd-Chiari Syndrome Masquerading as Paroxysmal Nocturnal Hemoglobinuria: a Case Report

1State Research Center – Burnasyan Federal Medical Biophysical Center of Federal Medical Biological Agency, Moscow, Russian Federation

2Russian Natiomal Research Medical Universiy named after N.I. Pirogov, Moscow, Russian Federation

Contact person: Slusar Anna Andreevna: ann.slusar@yandex.ru


Abstract
In this case report, the features of the course of the clinical presentation in a patient with paroxysmal nocturnal hemoglobinuria are analyzed; a life history, data from laboratory and instrumental examination methods are provided; the possibilities of modern methods of managing this pathology are discussed.

Keywords: ascites, Budd-Chiari syndrome, hepatic vein thrombosis, portal hypertension, paroxysmal nocturnal hemoglobinuria, PNH-clone, thrombocytopenia

For citation: Slusar AA, Vetkova KV. Budd-Chiari Syndrome Masquerading as Paroxysmal Nocturnal Hemoglobinuria: a Case Report. A.I. Burnasyan Federal Medical Biophysical Center Clinical Bulletin. 2023;4:48-51 (In Russian). DOI: 10.33266/2782-6430-2023-4-48-51


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Conflict of interest. The authors declare no conflict of interest.
Financing. The study had no sponsorship.
Contribution. Article was prepared with equal participation of the authors.
Article received: 15.11.2023.  Accepted for publication: 12.12.2023        

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